Desmoplastic Small Round Cell Tumor: A Case Report
Asian Oncology Research Journal,
Desmoplastic small round cell tumour is a very rare, highly malignant abdominal neoplasm of mesenchymal origin. Its non-specific symptoms at presentation and poor prognosis with a five year survival rate of 15% despite treatment make it a big challenge to manage. We wish to discuss a case of a young 17-year old male with abdominal pain and a palpable lump which was eventually diagnosed with desmoplastic round cell tumour.
- Desmoplastic small round cell tumor
- survival rate
- polyphenotypic differentiation
How to Cite
Kretschmar CS, Colbach C, Bhan I, Crombleholme TM. Desmoplastic small cell tumor: A report of three cases and a review of the literature. J Pediatr Hematol Oncol. 1996;18:293-298.
Lal DR, Su WT, Wolden SL, Loh KC, Modak S, La Quaglia MP. Results of multimodal treatment for desmoplastic small round cell tumors. Journal of Pediatric Surgery. 2005;40(1):251-5
Lae ME, Roche PC, Jin L, Lloyd RV, Nascimento AG. Desmoplastic small round cell tumor: a clinicopathologic, immunohistochemical, and molecular study of 32 tumors. The American Journal of Surgical Pathology. 2002; 26(7):823-35.
Hayes-Jordan A, Anderson PM. The diagnosis and management of desmoplastic small round cell tumor: A review. Current Opinion in Oncology. 2011;23(4):385-9.
Li G, Wang HT, Gao Y, Cui XJ, Zhang GZ. Primary abdominopelvic desmoplastic small round cell tumor: CT and correlated clinicopathologic features. Eur Rev Med Pharmacol Sci. 2014;18(18): 2670-7.
Yang JL, Xu WP, Wang J, Zhu XZ, Zhang RY. Desmoplastic small round cell tumor: a clinicopathologic study of 15 cases. Zhonghua bing li xue za zhi Chinese Journal of Pathology. 2005; 34(10):650-5.
Gil A, Gomez Portilla, Brun EA et al. Clinical perspective on desmoplastic small round-cell tumor Oncology. 2004;67:231-242.
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